Clinical variants of upper limbs deformities in children with arthrogryposis multiplex congenita

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From 2004 to 2012 the authors examined and treated 207 patients with upper limb deformities due to AMC. The age of children with AMC was from 5 months till 18 years. All upper limbs deformities due to AMC were deviated into 2 groups: isolated and complex forms. The isolated forms differ from each other by the level of damage of the spinal cord. There are 4 variants of isolated form with different clinical presentations (C6-7, C5-7, C5-T1, С6). The complex form presents AMC in combination with other pathology: Erb’s palsy, cerebral palsy and congenital upper limbs anomalies. The identification variants of upper limbs deformities in patients with AMC help to choose the optimal variant of treatment and predict the results of treatment.

About the authors

O. E. Agranovich

Turner Scientific and Research Institute for Children’s Orthopedics

Author for correspondence.
Russian Federation

O. L. Lakhina

Turner Scientific and Research Institute for Children’s Orthopedics

Russian Federation


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