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A multidisciplinary approach to treatment of patients with mucopolysaccharidosis allows to achieve good results. However, progressive spinal canal stenosis at the level of the craniovertebral junction, characteristic of this disease, leads to neurological signs, as well as a decrease in quality and length of life. The solution to this problem is a difficult challenge for spinal surgeons, as it is associated with a high risk of complications. There is also a wide range of opinions and approaches to the surgical treatment of this group of patients.

Using the referred Reporting Items for Systematic Review and Meta-Analysis» (PRISMA) protocol, a PubMed and eLIBRARY search was conducted using keywords to find articles describing patients with mucopolysaccharidosis who underwent surgical treatment for cervical stenosis. In this review, information on demographic parameters, surgical technique and the results of cervical stenosis treatment in patients with mucopolysaccharidosis is collected and analyzed.

About the authors

S. V. Kolesov

Priorov Central Institute of Traumatology and Orthopedics.

Author for correspondence.
10, ul. Priorova , 127299, Moscow. Russian Federation

L. K. Mikhaylova

Priorov Central Institute of Traumatology and Orthopedics.

10, ul. Priorova , 127299, Moscow. Russian Federation

D. A. Kolbovsky

Priorov Central Institute of Traumatology and Orthopedics.

10, ul. Priorova , 127299, Moscow. Russian Federation

V. S. Pereverzev

Priorov Central Institute of Traumatology and Orthopedics.

10, ul. Priorova , 127299, Moscow. Russian Federation


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